A RARE BRAIN TUMOUR- HYPOTHALAMIC PLEOMORPHIC XANTHOASTROCYTOMA IN A 11 YEAR OLD CHILD.

Background:Astrocytomas are the most common glial tumors of the central nervous system among the pediatric age group. Most of the childhood tumors occur infratentorially (medulloblastoma, astrocytoma and ependymomas ). Supratentorialastrocytomas are more likely to be low grade compared with their infratentorial counterpart. Pleomorphic xanthoastrocytomas are rare tumors accounting for only 1% of all astrocytomas. Despite its highly pleomorphic and bizarre looking cytology, it appeared to have a favorable prognosis and a relatively benign course. Its correct diagnosis is crucial. Conclusion: Pleomorphic Xanthoastrocytoma is a rare slowly growing tumour of childhood and young adults. Hypothalamus is a very rare site for pleomorphic xanthoastrocytoma. It can present with unusual sensory manifestations. Classical neuroimaging and histopathological characteristic are useful aids in diagnosis. Complete excision is the treatment of choice and gives very good results. A close follow up is always needed, as both recurrence and anaplastic transformation has been reported. Role of radiotherapy and chemotherapy is controversial except in malignant growth.