ASSOCIATION OF ASYMPTOMATIC NEUROENDOCRINE TUMOUR WITH RAPID-ONSET OBESITY, HYPOVENTILATION, HYPOTHALAMIC DYSFUNCTION, AND AUTONOMIC DYSFUNCTION (ROHHAD) SYNDROME.
- MBBS, Student at Faculty of Medicine at King Abdul Aziz University, Jeddah, Saudi Arabia, P. O. BOX. 80215.
- Professor of Paediatric Endocrinology, King Abdulaziz University Hospital, Paediatric Department, P. O. BOX 80215, Jeddah 21589, Saudi Arabia.MBBS, Student at Faculty of Medicine at King Abdul Aziz University, Jeddah, Saudi Arabia, P. O. BOX. 80215.
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Acknowledgment: We thank Dr. Mashael Saber for her excellent assistance and support in accomplishing this work. Disclosure: Authors have no conflict of interests, and the work was not supported or funded by any drug company. Word count: 1,183 words Number of tables: 2 Number of figures: 3 Consent for publication: Consent was obtained from the patients? legal guardian for this publication. Ethical approval and consent to participate: None applicable. Abstract: The rapid onset of obesity in the setting of hypoventilation, hypothalamic dysfunction and autonomic dysfunction constitutes the syndrome of ROHHAD-NET, with some cases presenting with a neuroendocrine tumour. It is a rare fatal disease due to respiratory failure that necessitates the early recognition and consequent provision of ventilatory support to improve outcome.
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[Asmaa Milyani, Abdulmoein Eid Al-Agha and Mashael Alzanbagi. (2017); ASSOCIATION OF ASYMPTOMATIC NEUROENDOCRINE TUMOUR WITH RAPID-ONSET OBESITY, HYPOVENTILATION, HYPOTHALAMIC DYSFUNCTION, AND AUTONOMIC DYSFUNCTION (ROHHAD) SYNDROME. Int. J. of Adv. Res. 5 (Aug). 917-922] (ISSN 2320-5407). www.journalijar.com
