08Jan 2019

LE SYNDROME DE PRADER WILLI A L AGE DE L ADOLESCENCE : DIFFICULTES DE PRISE EN CHARGE : A PROPOS DE DEUX CAS.

  • Service D?endocrinologie, Diabetologie Et Maladies Metaboliques, Chu Mohammed Vi, Hopital Errazi, Marrakech.
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Prader-Willi syndrome (PWS) is a rare disease first described in 1956. It is an important part of mental retardation related to a genetic cause and is one of the leading causes of syndromic obesity in children. It is responsible for physical, psychological and social disabilities of a particular gravity. The diagnosis is evoked on clinical elements and confirmed only by genetic analysis. The management of this disease is multidisciplinary and can be extremely difficult in the teenage age due to behavioral disorders and the total lack of autonomy of patients. We report the case of two patients followed in our training for the treatment of PraderWilli syndrome in adolescence with severe behavioral disorders.

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[Nassiba Elouarradi , Ghizlane Elmghari and Nawal Elansari. (2019); LE SYNDROME DE PRADER WILLI A L AGE DE L ADOLESCENCE : DIFFICULTES DE PRISE EN CHARGE : A PROPOS DE DEUX CAS. Int. J. of Adv. Res. 7 (Jan). 417-420] (ISSN 2320-5407). www.journalijar.com

Nassiba Elouarradi
Department of Endocrinology, Diabetology and Metabolic Diseases, Mohammed VI Hospital, Errazi Hospital, Marrakech, Morocco.

DOI:

Article DOI: 10.21474/IJAR01/8345      
DOI URL: https://dx.doi.org/10.21474/IJAR01/8345

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