27May 2019

MALIGNANT DEGENERATION IN SARCOMA OF A DERMATOFIBROSARCOMA OF DARIER FERRAND: A CASE STUDY.

  • Department of Plastic and Reconstructive Surgery, Mohammed VI CHU, Marrakech.
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Darier and Ferranddermatofibrosarcoma (DFS) is a cutaneous mesenchymal tumor of intermediate malignancy. It is a rare but not exceptional tumor, representing 0.1% of malignant skin tumors, slow growth, very high risk of local recurrence, but low metastatic potential. We report a case of malignant multi-recurrent degeneration in sarcoma of DarierFerranddermatofibrosarcoma in a 46 year-old patient , and this despite having evoked early diagnosis and performed a large surgical resection. This observation illustrates the frankly malignant but exceptional sarcomatous transformation.

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[Mohamed Elmehdi Sahibi , Mouna Ejjiyar, Mehdi ElGueouatri ,Bhihi Abdelkoddous, Driss Elamrani And Yassine Benchamkha. (2019); MALIGNANT DEGENERATION IN SARCOMA OF A DERMATOFIBROSARCOMA OF DARIER FERRAND: A CASE STUDY. Int. J. of Adv. Res. 7 (May). 1026-1030] (ISSN 2320-5407). www.journalijar.com

Mohamed Elmehdi SAHIBI
Doctor

DOI:

Article DOI: 10.21474/IJAR01/9130      
DOI URL: https://dx.doi.org/10.21474/IJAR01/9130

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