07Jul 2019

ADULT KAPOSIFORM HEMANGIOENDOTHELIOMA OF THE LEG COMPLICATED BY KASABAKH MERITT PHENOMENON.

  • Departement of stomatology and plastic surgery. Mohamed V teaching Armed Forced Hospital. Rabat.
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Kaposiform hemangioendothelioma is a rare, locally aggressive vascular neoplasm that mainly occurs during childhood . the tumor is often located on the skin but may be deeper. The development of KHE in adults is very rare, and its evolution towards KMP is exceptional. The KMP is defined as the combination of a deep thrombocytopenia and a vascular tumor, usually a KHE or a tuftted angioma. It is a life threatening pathology, because of the major risk of bleeding, and compression of vital structure. A multidisciplinary approach to treatment has to be employed.

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[Yassamina Ribag, Lahcen Khalfi, Kamal Fiqhi, Adil Ouardi, Issam MokfiI and Karim Elkhatib. (2019); ADULT KAPOSIFORM HEMANGIOENDOTHELIOMA OF THE LEG COMPLICATED BY KASABAKH MERITT PHENOMENON. Int. J. of Adv. Res. 7 (Jul). 530-537] (ISSN 2320-5407). www.journalijar.com

Abdelhafid ACHBOUK
departement of burn and plastic surgery

DOI:

Article DOI: 10.21474/IJAR01/9392      
DOI URL: https://dx.doi.org/10.21474/IJAR01/9392

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