LE SYNDROME DE LIMB BODY WALL COMPLEX A PROPOS DUN CAS ET REVUE DE LA LITTERATURE
- Service De Gynecologie Et Obstetrique, CHU Mohammed VI - Oujda,Faculte De Medecine Et De Pharmacie, Universite Mohammed Premier, Oujda, Maroc.
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Limb body wallcomplex (LBWC) is a rare poly malformative syndrome of unknownorigin, comprising major anomalies of the ventral body wall (thoracoabdominal) associatedwithother anomalies, includingthose of the limbsthatmay range frompositionaldeformity to agenesis, unusualcraniofacial malformations, and a variety of visceral anomalies thatinclude the heart, lungs, and genitourinary system. Twophenotypes are describeddepending on the feto-placentalattachment. We report a case of LBWC diagnosed post partum in a stillbornwith the following malformations: a large anterioromphalocele, spina bifida withmeningocele, and severescoliosis. The lowerlimbsappearedasymmetricalwithbilateral club feetassociatedwithpolydactyly. The stillbirthadheres to the placenta by a very short cord of 3 cm comprising 2 arteries and a vein.
[Aidi Asmae, El. Harcha Kamal, Taheri Hafssa, Saadi Hanane and Mimouni Ahmed (2022); LE SYNDROME DE LIMB BODY WALL COMPLEX A PROPOS DUN CAS ET REVUE DE LA LITTERATURE Int. J. of Adv. Res. 10 (May). 869-873] (ISSN 2320-5407). www.journalijar.com
Morocco
