30Dec 2024

THE LIMB BODY WALL COMPLEX: ABOUT TWO CASES - A RARE ANOMALY

  • Department of Obstetrics and Gynecology, Mohammed VI University Hospital Center, Faculty of Medicine and Pharmacy, Marrakech.
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Limb Body Wall Complex (LBWC) is a rare and severe congenital anomaly characterized by multiple malformations, including defects in the anterior body wall, internal viscera, spine, central nervous system, and limbs. This article presents two prenatal cases of LBWC diagnosed at 15 and 31 weeks of gestation. Both cases highlight key phenotypic variations, including ectopiacordis, thoracoabdominoschisis, and limb anomalies, with differing placental attachment patterns. Diagnostic considerations, including ultrasound and maternal serum markers, are discussed alongside insights into etiopathogenesis and the uniformly poor prognosis. These cases underscore the importance of early prenatal diagnosis to differentiate LBWC from other anomalies and guide appropriate management, typically medical termination of pregnancy due to the fatal nature of the condition.


[EL Mahfoudi A., Chqormani A., Abdallah A., Fakhir B., Ahlam B., Harrou K., Boukhani L., Asmouki H., Aboulfalah A. and Soummani A. (2024); THE LIMB BODY WALL COMPLEX: ABOUT TWO CASES - A RARE ANOMALY Int. J. of Adv. Res. (Dec). 1399-1405] (ISSN 2320-5407). www.journalijar.com


Aziz el mahfoudi

Morocco

DOI:


Article DOI: 10.21474/IJAR01/20152      
DOI URL: https://dx.doi.org/10.21474/IJAR01/20152