CASE REPORT PROSTHETIC REHABILITATION IN ECTODERMAL DYSPLASIA

Background: Ectodermal dysplasia (ED) represents a group of rare, inherited disorders characterized by developmental anomalies in structures derived from the ectoderm. Hypohidrotic ED, the most common type, often presents with oligodontia or anodontia, posing significant functional and psychological challenges in children. Case Report: This case describes a 5-year-old boy with hypohidrotic ectodermal dysplasia presenting with oligodontia, dry skin, sparse hair, and typical facial features such as a saddle nose and thick everted lips. The child exhibited difficulty in mastication, speech, and an inability to sweat. Clinical and radiographic evaluation revealed the presence of only four primary second molars and a few developing permanent molars. A multidisciplinary treatment approach was adopted, and early prosthetic rehabilitation with removable partial dentures was undertaken to restore function, esthetics, and psychosocial confidence. Conclusion: Early prosthetic management in pediatric patients with ectodermal dysplasia is crucial for enhancing oral function, supporting normal craniofacial growth, and improving quality of life. Timely dental intervention addresses physical challenges and plays a vital role in the child's emotional and psychological development.