RIGHT DIAPHRAGMATIC DOME HERNIA (DDH), A POOR PROGNOSIS: A CHALLENGE, HOPE AND REALITY- A CASE REPORT

Diaphragmatic dome hernia (DCH) is a malformation of the diaphragm characterized by an embryonic defect of one (or both) diaphragmatic dome(s) The diagnosis is most often made during an antenatal screening ultrasound In the case of an isolated form, prenatal evaluation of the postnatal prognosis of children with diaphragmatic dome hernia (DDH) is necessary and is currently more accurate thanks to prognostic factors: LHR, position of the liver and total lung volume.Although the prognosis has improved over the last 20 years thanks to prenatal diagnosis, advances in surgery and management in neonatal intensive care, some children still develop complications, especially those with a severe form of the disease and/or the orifice in the diaphragm is in the right side.

Methodology: We present a case of right CDH, right CDH overall with a poorer prognosis than left hernias, and through this case we present the methods of antenatal evaluation, prognostic factors, the main developments in surgical management, immediate postnatal management or long-term monitoring and the evolution of recommendations.