An atypical presentation of acrokeratosis verruciformis of Hopf- A case report

Acrokeratosisverruciformis (AKV) of Hopf is a rare genodermatosis of keratinization disorder. It was first described by Hopf in 1931. It is usually present at birth and more common in males (M:F=5:1.3).Most common mode of inheritance is autosomal dominant. It is characterized by multiple flat topped skin colored wartykeratotic papules mainly over the dorsa of the hands and feet. We reported an atypical sporadic case of widespread AKV with minimal acral parts involvement in a 17-year-old girl due to its rarity.