Title: A Dental Perspective on the Rare Disorder of Acromesomelic Dysplasia - A Case Report.

Introduction: Acromesomelic dysplasia, the Maroteaux type is listed as a “rare disease” by the office of rare diseases (ORD) of the National Institute of Health (NIH). This means that acromesomelic dysplasia, Maroteaux type (AMDM), or a subtype of acromesomelic dysplasia affects less than 200,000 people. Acromesomelicdysplasiasare skeletal disorders that disproportionately affect the middle and distal segments of the appendicular skeleton. As with the appendicular features, the vertebral features become more pronounced throughout childhood. The pelvis has a typical configuration, and the cranium may demonstrate frontal bossing, with a normal head circumference, hypoplastic maxilla and malocclusion. Case report:The following case report discusses the medical and dental findings of acromesomelic dysplasia and their subsequent management. Conclusion: Disorders like acromesomelic dysplasia have rarely been documented for any oral findings. Further documentation of such cases would be essential in establishing the full scope of the oral features. The findings enlisted here suggest that early preventive measures and intercepting any developing malocclusions would suffice the promotion of good oral health during infancy and childhood.