02Feb 2018

MYOFIBROMATOSE INFANTILE: A PROPOS D UN CASINFANTILE MYO FIBROMATISIS : CASE REPORT.

  • Service dAnatomie et Cytologie Pathologiques. Hpital des spcialits. CHU Rabat.
  • Service dORL et de Chirurgie maxillo-faciale. Hpital des spcialits. CHU Rabat.
  • Facult de Mdecine et de Pharmacie de Rabat (FMPR). Auteur principal: Amine Kessab.
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Introduction: Infantile myofibromatosis (IM) is a rare benign mesenchymal tumor. It performs various clinical aspects. This is the most common fibromatosis of the child; it is characterized by a proliferation of fibroblasts and myofibroblasts with particular perivascular disposition. Methods: We report a case of a male child presented with a cervical mass since birth. Clinical examination showed a well circumscribed mass in the right cervical region. The Tomography objectified a benign look mass embedded in the sterno-mastoid and surgical resection was decided. Results: The mass was resected at the age of 2 years and 4 months. Pathological examination with immunohistochemical study allows to retain the diagnosis of infantile myofibromatosis. Conclusion: IM is a rare tumor that shows clinicopathological characteristics well defined. It should be considered as a differential diagnosis in any child with a solitary or multiple mesenchymal tumor, particularly that occurring during the first two years of life. Through this observation pathological, clinical, etiopathogenic and cytogenetic characteristics of this infantile tumor are described.

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[Amine Kessab, Karima Laadam, Saoud Idriss, Mouna khmou, El Ayoubi Ali, Benbouzid Mohamed Anass, Esskalli Leila and Nadia Cherradi. (2018); MYOFIBROMATOSE INFANTILE: A PROPOS D UN CASINFANTILE MYO FIBROMATISIS : CASE REPORT. Int. J. of Adv. Res. 6 (Feb). 7-13] (ISSN 2320-5407). www.journalijar.com

Amine Kessab
(1) Service d’Anatomie et Cytologie Pathologiques. Hôpital des spécialités. CHU Rabat.

DOI:

Article DOI: 10.21474/IJAR01/6402      
DOI URL: https://dx.doi.org/10.21474/IJAR01/6402

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