HYDRANCEPHALY : RARE ENTITY WITH INCIDENCE LESS THAN 1 IN 10000 LIVE BIRTHS

Hydranencephaly is a rare entity with incidence of 1 in 10000 live births and is characterized by near total absence of cerebral cortex and basal ganglia which are replaced by cerebrospinal fluid. Various aetiologies of hydranencephaly have been suggested which include: Infarction, leukomalacia, diffuse hypoxic-ischemic brain necrosis, intrauterine infections leading to necrotizing vasculitis. Ultrasonography, Computed Tomography and Magnetic Resonance Imaging  can easily detect and diagnose hydranencephaly. We present a case of 2-month-old term infant diagnosed with hydranencephaly on computed tomography.