A RARE CASE REPORT OF OHVIRA SYNDROME IN A MENTALLY RETARDED GIRL

Obstructed Hemi vagina & Ipsilateral renal agenesis or Herlyn werner Wunderlitch syndrome is a rare Mullerian duct anomaly with uterus didelphys, Unilateral Obstructed Hemi vagina & Ipsilateral renal agenesis. Patients can usually presents soon after menarche and mayshow non - specific and variable symptoms with resultant delay in diagnosis. The most common presentation is dysmenorrhoea , abdominal mass in the lower abdomen secondary to hematocolpos and or haematometra. Here presenting a case of 14 years old mentally retarded female presented with pain abdomen & mass per abdomen and was diagnosed as OHVIRA syndrome based on Ultrasonography & MRI pelvis. She was treated with hemi vaginal septal resection and was under follow up.