CASE REPORT EHLER DANLOS RARE CAUSE OF PULMONARY HYPERTENSION

Ehler Danlos syndrome is an inherited disorder that affect theconnectiv e tissue,recently Ehler Danlos syndrome subdivided in different 13 to 14 types. Ehler Danlos syndrome is not a direct cause of pulmonary hypertension but association between the two condition may occur.We presented a rare case of pulmonary hypertension as first presentation of Ehler Danlos syndrome in years male who presented with progressive dyspnea.